J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere

Instructional Notes:

J84.170
Description: Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere
Code First:
- underlying disease, such as:
- lung diseases due to external agents (J60-J70)
- rheumatoid arthritis (M05.00-M06.9)
- sarcoidosis (D86.-)
- systemic connective tissue disorders (M30-M36)
Inclusion Term:
- Progressive fibrotic interstitial lung disease
↓
J84.17
Description: Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
↓
J84.1
Description: Other interstitial pulmonary diseases with fibrosis
Exclude1:
- pulmonary fibrosis (chronic) due to inhalation of chemicals, gases, fumes or vapors (J68.4)
- pulmonary fibrosis (chronic) following radiation (J70.1)
↓
J84
Description: Other interstitial pulmonary diseases
Exclude1:
- drug-induced interstitial lung disorders (J70.2-J70.4)
- interstitial emphysema (J98.2)
Exclude2:
- lung diseases due to external agents (J60-J70)
Code Also: [', if applicable, associated condition']
↓
J80-J84
Description: Other respiratory diseases principally affecting the interstitium (J80-J84)
↓
J00-J99
Description: Diseases of the respiratory system
Exclude2:
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- smoke inhalation (T59.81-)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Notes:
- When a respiratory condition is described as occurring in more than one site and is not specifically indexed, it should be classified to the lower anatomic site (e.g. tracheobronchitis to bronchitis in J40).
Use Additional Code:
- code, where applicable, to identify:
- exposure to environmental tobacco smoke (Z77.22)
- exposure to tobacco smoke in the perinatal period (P96.81)
- history of tobacco dependence (Z87.891)
- occupational exposure to environmental tobacco smoke (Z57.31)
- tobacco dependence (F17.-)
- tobacco use (Z72.0)